Bednar tumor is a rare variant of dermatofibrosarcoma protuberans (DFSP). However, the presence of pigment-bearing cells distinguishes it from DFSP. We report a case of Bednar tumor occurring in a 52-year-old white woman and review the typical clinical and histopathologic findings. To our knowledge, this is the second reported case of Bednar tumor successfully treated with Mohs micrographic surgery. The patient remains free of recurrence 5 years after treatment. Because of the clinical similarity between Bednar tumor and DFSP, we recommend Mohs micrographic surgery for treatment of this rare tumor.